The paper describes a clinicoanatomic case of two deceased neonates with fibromyxomatous hyperplasia of mitral and tricuspid valve leaflets with vascular malformations of the lung, lower extremity, spermatic cord, and thrombotic and hemorrhagic complications. The cases are considered in the context of congenital connective tissue dysplasia.
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Gardner Syndrome With Unusual Maxillofacial Manifestation.
J Craniofac Surg
July 2016
Department of Diagnosis and Surgery, Araraquara Dental School, São Paulo State University (UNESP), Araraquara, SP, Brazil.
Gardner syndrome is a rare autosomal-dominant condition characterized by the presence of intestinal polyposis, multiple osteomas, and tumors of the hard and soft tissues. This paper describes a patient of Gardner syndrome with unusual maxillofacial manifestation with presence of fibromyxomatous injury in jaw, coronoid hyperplasia, and multiple osteomas diffusely distributed in the craniomaxillofacial skeleton. Imaging examinations have identified craniofacial manifestations and the patient was referred to the gastroenterologist who confirmed the diagnosis of Gardner syndrome.
View Article and Find Full Text PDFPeripheral odontogenic fibroma is considered a gingival tumor characterized by a proliferation of relatively cellular fibrous or fibromyxomatous connective tissue which exhibits variable amounts of odontogenic epithelium and sometimes foci of calcification in the form of dentinoid, cementicles, or bone. It is considered the extraosseous counterpart of central odontogenic fibroma. This lesion usually is presented as a focal swelling in the gingiva, occurring in a wide age range, and the anterior region of the gingiva is the most frequent anatomic site.
View Article and Find Full Text PDFThe paper describes a clinicoanatomic case of two deceased neonates with fibromyxomatous hyperplasia of mitral and tricuspid valve leaflets with vascular malformations of the lung, lower extremity, spermatic cord, and thrombotic and hemorrhagic complications. The cases are considered in the context of congenital connective tissue dysplasia.
View Article and Find Full Text PDFA rare case of the combination of fibromyxomatous hyperplasia of the valves and postmyocarditis elastofibrosis is described in a child who died at the age of 1 month and 26 days. The genesis of the heart pathology may be attributed to the carditis at the early fetal period. A possible source of the carditis could be a focus of chronic inflammation in the maternal internal genitalia.
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