Prenatally diagnosed right ventricular outpouchings: a case series and review of the literature.

Pediatr Cardiol

Department of Obstetrics and Gynecology, Division of Maternal-Fetal Medicine, University of Michigan Medical Center, L4835 Mott, 1500 East Medical Center Drive, Box 0276, Ann Arbor, MI 48109-0276, USA.

Published: August 2009

Congenital right ventricular aneurysms and right ventricular diverticula are rare forms of congenital heart disease for which little information exists regarding optimal management, natural history, or prognosis. With advancements in prenatal cardiac evaluation and ultrasound, the reported frequency of these lesions, as well as a better understanding of the natural history of this form of congenital heart disease, is likely to evolve. We present three cases of fetal right ventricular aneurysms/diverticula diagnosed at our institution, along with a review of the current literature. We describe the pre- and postnatal courses as well as suggest counseling and management strategies.

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http://dx.doi.org/10.1007/s00246-009-9425-2DOI Listing

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