Background And Objectives: Von Recklinghausen's disease is a neurogenetic disease due to chromosome 17 abnormality. This report aimed at describing the anesthetic approach for Von Recklinghausen's disease patient submitted to urgency orthopedic surgery.

Case Report: Female patient, 28 years old, with Von Recklinghausen's disease, submitted to emergency orthopedic surgery under spinal block. There have been no complications both in the intraoperative period and in the post-anesthetic care unit. Patient was discharged 4 days later.

Conclusions: Spinal block was possible in this case with no need for airway handling.

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http://dx.doi.org/10.1590/s0034-70942005000600008DOI Listing

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