AI Article Synopsis
- * It highlights a less common association between congenital hepatic fibrosis and autosomal dominant polycystic kidney disease (ADPKD), noting there is limited documentation on this.
- * The report focuses on a specific case of a child with neonatal hypertension from ADPKD who later developed portal hypertension due to CHF in childhood, leading to a review of this rare connection.
Article Abstract
The association of congenital hepatic fibrosis (CHF) with autosomal recessive polycystic kidney disease (ARPKD) is well known and occurs in approximately 50% of cases. However the association of CHF with autosomal dominant polycystic kidney disease (ADPKD) is less well known and less well documented. We report a child with neonatal onset of hypertension due to ADPKD who later develops portal hypertension due to CHF in childhood. A review of this rare association follows.
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