Introduction: cystinuria is a severe form of renal which is exposed the patient at multiple recurrent.
Objective: Report and identify the clinical and biochemical characteristic of cystinuria in Tunisian region.
Methods: It is a study of 25 cases of cystinuria, concerning at 16 adults and 9 children from 1995 to 2006. Cystinuria is recognized on the basis of spectrophotometric analysis of the stones (24/1586), by study of urinary crystals completed with brands test (5 cases) or by the two types of explorations.
Results: the frequence of cystinuria is 1.5% (25/1586). 89% stones were renal and 23% were bilateral. The stones have a diameter between 15/30 mm and classified type V at morphology.
Conclusion: Our data will improve the management based on early diagnosis, regular follow up and respect of dietetic rules.
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