Central neurofibromatosis. Case report and review of the literature.

Eur Neurol

Department of Neurosurgery, Hacettepe University Hospitals, Ankara, Turkey.

Published: September 1991

An unusual case of central neurofibromatosis associated with a unilateral acoustic neuroma, multiple intracranial meningiomas, spinal neurofibroma and visceral involvement is presented. The progressive clinical course of this syndrome is described and discussed with a review of the relevant literature.

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http://dx.doi.org/10.1159/000116676DOI Listing

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