A "hyperextensive" review of Ehlers-Danlos syndrome.

Cutis

Dermatology and Pediatrics, New Jersey Medical School, Newark 07103-2714, USA.

Published: October 2008

AI Article Synopsis

  • Ehlers-Danlos syndrome (EDS) is a group of connective tissue disorders with symptoms including hyperextensibility, joint hypermobility, and skin fragility.
  • There are six main types of EDS, each varying in symptoms and severity.
  • Physicians need to recognize that prominent skin signs in EDS indicate a significant underlying systemic disorder.

Article Abstract

Ehlers-Danlos syndrome (EDS) is a heterogeneous group of connective tissue disorders characterized by hyperextensibility, delayed wound healing, joint hypermobility, thin skin, easy bruising, tissue fragility, "cigarette-paper" scarring over bony prominences, mitral valve prolapse, and other findings. There are 6 main types of EDS. Regardless of presentation as a chief concern or an incidental finding, physicians should be aware that the prominent skin findings of EDS are cutaneous signs of an important systemic disorder.

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