Renal lymphangiectasia is a rarely reported disorder of lymphatic malformation. Although benign, it may lead to hypertension and renal failure in undetected or undiagnosed cases. Adult polycystic kidney disease is a close mimic. We herewith present a rare case of bilateral renal lymphangiectasia that was strongly suspected on computed tomographic (CT) scan and confirmed by aspiration cytology. Awareness about this condition will result in early diagnosis, early treatment and reduced morbidity.
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Feinberg Cardiovascular and Renal Research Institute, Northwestern University Feinberg School of Medicine, Chicago, IL.
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From the Department of Surgery (Ayed), from the Department of Pathology (Sohail, Rizvi), College of Medicine, University of Bisha; and from the Department of Urology (Alwadai), King Abdullah Hospital, Ministry of Health, Bisha, Kingdom of Saudi Arabia.
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- Renal lymphangiectasia (RL) is a rare condition characterized by dilated lymphatic vessels leading to cysts in various kidney locations, and its understanding largely stems from individual case reports.
- The condition can be genetic or acquired, affects individuals of any gender or age, and often presents as abdominal or flank pain, being either focal or diffuse and unilateral or bilateral.
- Diagnosis relies on imaging techniques, and while treatment is typically conservative, there is a need for long-term monitoring for complications like hypertension and renal vein thrombosis; a case of bilateral RL is discussed alongside a literature review.
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Imaging of Perirenal and Intrarenal Lymphatic Vessels: Anatomy-based Approach.
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March 2024
From the Department of Radiology (H.T., A.I., T.A.P., N.T.) and Department of Medicine, Division of Rheumatology (Y.S.), Mayo Clinic, 200 First St SW, Rochester, MN 55905; Department of Radiology, Okayama City Hospital, Okayama, Japan (T.T.); Department of Radiology, Jichi Medical University, Tochigi, Japan (S.M.); Department of Diagnostic and Interventional Radiology, University of Tsukuba, Ibaraki, Japan (M.M.); and Department of Radiology, Mayo Clinic, Scottsdale, Ariz (A.K.).
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