AI Article Synopsis
- The case report discusses a 17-year-old patient diagnosed with Mayer-Rokitansky-Kuster-Hauser syndrome, presenting with primary amenorrhea and associated anomalies, including a pelvic ectopic kidney and a perirenal cyst.
- Imaging revealed no uterus and a cystic lesion in the right adnexal area, along with a centrally located ectopic kidney, while hormone levels and tumor markers remained normal.
- During laparoscopic surgery, the absent uterus and fallopian tubes were confirmed, and an 8 x 11 cm perirenal cyst containing endometrial tissue was surgically removed from the retroperitoneal area.
Article Abstract
In this case report, a Mayer-Rokitansky-Kuster-Hauser syndrome with pelvic ectopic kidney and a perirenal cyst with endometrial tissue inside is demonstrated. A 17 year old patient admitted with primary amenorrhea. Pubertal stages were completed. In pelvic ultrasonography; uterus could not be detected, a 6 x 11 cm sized cystic lesion was seen on the right adnexal area. A centrally located 5.5 x 9 cm sized ectopic pelvic kidney was detected. Hormones and tumor markers were normal. Laparoscopy was planned. In the laparoscopic observation, uterus and both tubes could not be detected, ovaries were normal. There was a 6 x 7 cm sized cyst located in the retroperitoneal area, the origin of the cyst could not be identified. Laparatomy was considered, retroperitoneal space was entered, an 8 x 11 cm sized smooth contoured perirenal cyst adjacent to the pelvic kidney was detected. Cyst was extirpated. The pathology result was reported to include endometrial tissue and hemorrhage inside.
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