Pseudoprune belly syndrome; its' associations and management challenge in a developing country: a case report.

Background: Pseudo prune belly syndrome is an incomplete expression of the triad syndrome. Its incidence is poorly documented worldwide. We are not aware of any documented cases in Nigeria in recent times. Diagnosis is clinical; however, ultrasound scan plays key role in the overall assessment of the patient.

Method: It is a report of an 8 day old boy who had pseudo prune belly syndrome with associated micro colon and rectal atresia managed at the Ahmadu Bello University Teaching Hospital (ABUTH), Zaria, in October, 2005.

Conclusion: Management of this patient was challenging due to lack of frozen section facility parenteral nutrition and finance. Awareness of the associated conditions and how to manage them is emphasized for good outcome.