A 54-year-old male presented with a painful, erythematous, fissured plaque involving the left groin and adjacent scrotal skin. In addition, he exhibited white longitudinal bands and ridges on his fingernails, more prominent on thumb nails. Skin biopsy from the left groin confirmed the diagnosis of chronic familial benign pemphigus (Hailey-Hailey disease). To the best of our knowledge, this is the first case report from India in which we have described nail involvement in Hailey-Hailey disease.
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