Purpose: Periosteal osteosarcomas are rare cartilage-rich bone tumours characterized by a juxtacortical eccentric position and are normally regarded oncologically as of intermediate to high grade.Their low incidence is mirrored by a small number of reported cases in the world literature. While there is general agreement that wide surgical excision is required, there is a paucity of evidence regarding adjuvant therapy. Previous reports have not indicated any consistent approach to this to allow appraisal.

Patients And Methods: We report 17 cases treated at our centre over 16 years. Our policy was to use chemotherapy when the tumour showed any features of high grade.

Results: To date, no deaths have resulted from recurrence or metastasis of the tumour although there have been two deaths from other causes.

Discussion: Comparison of survival with existing studies is made to draw conclusions regarding future treatment of this condition in terms of surgical and adjuvant approaches.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2395495PMC
http://dx.doi.org/10.1080/1357714021000066368DOI Listing

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