An 18-month-old female presented with an abdominal tumor mass which on morphological, immunohistological and ultrastructural examination was found to be a malignant fibrous histiocytoma. This soft tissue sarcoma is rarely encountered in childhood. Treatment in this case consisted of surgical tumor debulking with pre- and post-operative chemotherapy. The child is well and free of detectable tumor at 23 months after diagnosis.
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