AI Article Synopsis
- Wegener's granulomatosis (WG) is a complex disease that causes inflammation and damage to small and medium blood vessels, affecting multiple organs with symptoms like tissue necrosis.
- Patients with WG may experience joint issues early on, even before more common symptoms appear, and there's a risk of developing pneumothorax due to complications like ruptured sub-pleural nodules.
- The paper highlights the significance of recognizing early joint involvement and the potential for pneumothorax to encourage timely diagnosis and treatment to prevent severe complications.
Article Abstract
Wegener's granulomatosis (WG) is a multiorgan system disease of unknown etiology characterized by granulomatous inflammation, tissue necrosis, and variable degrees of vasculitis in small- and medium-sized blood vessels. In patients with WG, the musculoskeletal system can be involved before other typical symptoms of the disease. Also in WG, pneumothorax can develop as a rare complication. In this paper, we report a case with WG who had early articular involvement in the absence of classic features of illness and had pneumothorax which resulted from the rupture of the sub-pleural nodule. The aim of this work is to increase the awareness of early articular involvement in WG and the pneumothorax possibility especially in cases with cavitated nodules closure to pleura. This case emphasizes that early diagnosis and treatment is very important in avoiding further complications.
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| http://dx.doi.org/10.1007/s10165-007-0007-y | DOI Listing |
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