[One-stage surgical treatment of congenital blepharophimosis syndrome].

Zhongguo Xiu Fu Chong Jian Wai Ke Za Zhi

Department of Maxillo-Facial Surgery. Plastic Surgery Hospital of Peking Union Medical College, Chinese Academy of Medical Sciences, Beijing, 100041, PR China.

Published: November 2007

AI Article Synopsis

  • The study investigates the effectiveness of combining medial and lateral canthoplasty with blepharoptosis correction in patients with congenital blepharophimosis syndrome.
  • From January 2002 to May 2006, 26 patients aged 3 to 35 underwent the procedure, with significant improvements in eyelid dimensions and muscle function post-surgery.
  • All patients expressed satisfaction with the results after a follow-up period of 3 months to 4 years, indicating that this one-stage surgical approach is a viable treatment option.

Article Abstract

Objective: To explore the clinical effect of combining medial and lateral canthoplasty with blepharoptosis correction at one-stage for congenital blepharophimosis syndrome.

Methods: From January 2002 to May 2006, 26 patients (52 sides) with congenital blepharophimosis syndrome were treated. There were 16 males and 10 females, aging from 3 to 35 years (mean 8.5 years). They were all bilateral blepharoptosis significantly. The palpebral muscle force was 0-3 mm; the transverse dimension and vertical dimension of the palpebral tissue were 13-22 mm and 2-4 mm; the intercanthal distance was 33-44 mm; the levator function was 1-3 mm.

Results: Twenty-six patients underwent medial canthoplasty and blepharoptosis correction of them. 12 patients were also given lateral canthoplasty at one-stage. The postoperative transverse dimension and vertical dimension of the palpebral tissue were 6-8 mm and 24-32 mm, respectively. The intercanthal distance was 29-34 mm. The levator function was 4-6 mm. The supratarsal fold in the upper lid was natural. With a follow up of 3 months to 4 years. all patients were satisfied with their results.

Conclusion: One-stage surgical treatment of combining medial and lateral canthoplasty with blepharoptosis correction can achieve good result for blepharophimosis syndrome with a shortened treatment time.

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