Angiomyofibroblastoma of the retroperitoneum: a case report.

Background: Angiomyofibroblastoma is a rare soft tissue neoplasm that presents most frequently in the genital region of young to middle-aged women.

Case: A 28-year-old woman presented with nausea, vomiting and pelvic pain. Computed tomography revealed a well-circumscribed, brightly enhancing pararectal mass in the retroperitoneum. A core needle biopsy suggested the diagnosis of angiofibromyoblastoma. Due to the highly vascular nature of the lesion, the patient underwent angiographically guided embolization in an effort to minimize surgical blood loss. This was followed by exploratory laparotomy and resection of the mass.

Conclusion: This case illustrates an unusual presentation of angiomyofibroblastoma in the pelvic retroperitoneum and its management with preoperative selective embolization, which may have contributed to the minimal blood loss at the time of resection.