This is the first case report of successful anesthesia management in a high-risk neurological procedure in a patient with PHACE syndrome. PHACE syndrome is rare but an important clinical entity. Anesthesiologists should be aware of the neurological, otolaryngogical, and vascular risk associated with this syndrome.
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Contralateral oculomotor nerve palsy associated with PHACES syndrome.
J AAPOS
December 2024
Ophthalmology and Visual Sciences, University of British Columbia, Vancouver, Canada.
A 13-month-old boy presented to the pediatric ophthalmology clinic at BC Children's Hospital for strabismus assessment. On examination he had a right facial hemangioma, left ptosis, and left exotropia and hypotropia. Magnetic resonance imaging and magnetic resonance angiography of his head demonstrated posterior cerebral artery tortuosity producing mild mass effect on the left oculomotor nerve.
View Article and Find Full Text PDFMost common congenital syndromes with facial asymmetry: A narrative review.
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Department of Oral Pathology, Wroclaw Medical University, Poland.
Symmetry is present in various aspects of everyday life. A symmetrical face is considered attractive, whereas a lack of facial symmetry is regarded as a source of functional and aesthetic problems. Most of the people exhibit slight asymmetries, but some of them reveal severe asymmetries.
View Article and Find Full Text PDFPHACEing a challenging diagnosis: Should we expand the phenotype?
J Med Imaging Radiat Oncol
October 2024
Paediatric Neurology/Neurogenetics Units, Monash Health, Melbourne, Victoria, Australia.
Article Synopsis
- PHACE syndrome is a complex prenatal condition that can have significant health implications, often identified through specific signs observed in prenatal imaging.
- The 'tilted telephone receiver' sign suggests a strong link to PHACE, but recent cases show it can also appear in less severe forms, prompting discussions about expanding how we recognize this syndrome.
- A particular case with mild symptoms resembling PHACE did not actually result in the condition after birth, indicating that expanded criteria for diagnosis could lead to incorrect negative predictions for affected pregnancies.
PHACE syndrome: A review.
Semin Pediatr Neurol
October 2024
Department of Neurology, Dell Medical School, The University of Texas at Austin, 1601 Trinity St., Bldg. B, Stop Z0700, Austin, TX 78712, United States. Electronic address:
Article Synopsis
- PHACE syndrome is a neurocutaneous disorder characterized by brain abnormalities, facial hemangiomas, and various arterial and cardiac issues.
- While visible hemangiomas are the most prominent symptom, serious complications like aortic anomalies and strokes can arise, making early identification crucial.
- The article reviews important clinical features, diagnostic approaches, and management strategies, highlighting the significance of this condition for pediatric neurologists.
Infantile hemangioma precursor lesions on day of life 1: A Mayo Clinic retrospective case series.
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Department of Dermatology, Mayo Clinic, Rochester, Minnesota, USA.
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- Infantile hemangiomas (IHs) are common vascular tumors that typically develop during the first few weeks of an infant's life, but the precursor lesions can be mistaken for other conditions.
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