Mastocytosis is a group of disorders characterized by the accumulation of mast cells in different tissues and organs. The skin is the most frequently involved organ (90% of cases) where mastocytosis may show a heterogenic clinical expression. Anetodermic lesions are an unusual clinical presentation of mastocytosis. We report a case of anetodermic mastocytosis in a 26-year-old man, with sparse lesions and a benign course. PUVA therapy obtained excellent results in this case. Darier's sign should be investigated in patients with anetodermic lesions of unclear origin in order to exclude cutaneous mastocytosis.
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Coexistence of two types of clinical lesions in childhood-onset mastocytosis.
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The vast majority of mastocytosis appear in childhood, urticaria pigmentosa (UP) and mastocytomas being the most common types. Terms such as "xanthelasmoid mastocytosis", "pseudoxanthomatous mastocytosis" or "nodular mastocytosis" have been introduced in the literature to describe the presence of yellowish papular or nodular lesions. We describe two children with cutaneous mastocytosis showing yellowish lesions in combination with other skin lesions.
View Article and Find Full Text PDFAnetodermic mastocytosis: response to PUVA therapy.
J Dermatolog Treat
July 2007
Department of Dermatology, Hospital Juan Canalejo, La Coruña, Spain.
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View Article and Find Full Text PDFSecondary anetoderma associated with mastocytosis.
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January 2007
Department of Allergy, Attikon Hospital, University of Athens, Athens, Greece.
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