Failure of automatic involuntary respiration with preservation of voluntary respiratory drive (Ondine's curse) is a rare occurrence which has been reported following a variety of morphologic lesions near respiratory centers in the lower brainstem. We report the case of a 39-year-old woman with a syndrome of fulminant respiratory failure with features of Ondine's curse in whom neuropathologic examination disclosed a preexisting malformation of the lower brainstem, as well as acute local subarachnoid bleeding. Mechanisms in the present case are discussed and a review of similar cases published so far is given. The necessity of sound investigation, including neuropathologic studies in cases of sudden unexplained death, is underlined.
Download full-text PDF |
Source |
|---|---|
| http://dx.doi.org/10.1097/01.paf.0000257396.79742.e9 | DOI Listing |
Publication Analysis
Top Keywords
Similar Publications
Central sleep apnea as an initial presentation of small cell lung carcinoma with anti-Hu antibody-related paraneoplastic neurologic syndrome.
Respirol Case Rep
December 2024
Division of Critical Care Medicine, Department of Internal Medicine National Cheng Kung University Hospital Tainan Taiwan.
Anti-Hu antibody-related paraneoplastic neurologic syndrome (PNS), a rare disease primarily associated with small cell lung carcinoma, is characterized by diverse neurologic manifestations. Central sleep apnea, although rare, is specific to anti-Hu antibody-related PNS. Herein, we present a case of out-of-hospital cardiac arrest attributed to hypercapnic central sleep apnea and detail the subsequent workup that revealed anti-Hu brainstem encephalitis.
View Article and Find Full Text PDFCytomegalovirus and varicella zoster virus coinfection-associated central hypoventilation syndrome (Ondine's Curse).
eNeurologicalSci
March 2024
LSUHSC Neurology Residency Program, United States of America.
Central hypoventilation syndrome (CHS) is a rare condition resulting from damage to the respiratory centers in the central nervous system (CNS). It can be congenital or acquired and can cause hypoventilation, inadequate gas exchange, and respiratory failure, often during sleep but sometimes even while awake. CHS can lead to respiratory failure and life-threatening complications if not identified promptly.
View Article and Find Full Text PDF"You Sleep, You Die": A Rare Clinical Case of Ondine's Curse after Posterior Fossa Surgery.
Case Rep Surg
September 2023
Department of Neurosurgery, Al Tadawi Specialty Hospital, Dubai, UAE.
Ondine's curse is a rare condition in which breathing is preserved while awake, but there is absence of autonomic control of ventilation. It is a potentially fatal complication that may result rarely from surgery in posterior fossa in area close to respiratory centers. We describe a patient with posterior fossa hemangioblastoma who underwent subtotal resection via telovelar approach and developed acquired Ondine's curse postoperatively.
View Article and Find Full Text PDFCase report: Central alveolar hypoventilation in a survivor of cardiopulmonary arrest.
Front Neurol
August 2023
Department of Critical Care Medicine, University of Pittsburgh Medical Center, Pittsburgh, PA, United States.
Introduction: Ondine's curse is a rare respiratory disorder that is characterized by central alveolar hypoventilation (CAH) during sleep. It is most commonly congenital. However, it can also be acquired very rarely.
View Article and Find Full Text PDFOndine's curse: clinical presentation with diaphragmatic pacing and spontaneous respiratory recovery. Illustrative case.
J Neurosurg Case Lessons
May 2023
Departments of1Neurological Surgery.
Background: The complexity of posterior fossa surgery can often lead to rare complications due to the anatomy involved. Vestibular schwannoma resection is a common pathology in the posterior fossa, often requiring surgical intervention. Given the proximity of this space to the brainstem, cranial nerve VII/VIII complex, and posterior inferior cerebellar artery (PICA), neurovascular complications are not infrequent.
View Article and Find Full Text PDFWant AI Summaries of new PubMed Abstracts delivered to your In-box?
Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!