Bilateral prominent schwalbe ring in the anterior chamber in a patient with axenfeld-rieger syndrome and megalocornea.

Purpose: To report the unusual presentation of bilateral Schwalbe rings suspended in the anterior chambers of a patient with Axenfeld-Rieger syndrome.

Methods: A 37-year-old man with bilateral decreasing visual acuity underwent slit-lamp examination, dark room gonioscopy, and photographic documentation.

Results: Prominent bilateral Schwalbe rings and peripheral iridocorneal strands were observed in both anterior chambers. No systemic abnormalities were found.

Conclusions: The position of the Schwalbe ring in patients with Axenfeld-Rieger syndrome can vary in appearance from almost normal to displaced markedly. It remains to be seen whether these variations reflect genetic differences.