Objective: This retrospective case series analyzes two cases of hemangioblastomas in the cervicomedullary junction.

Methods: A survey of the pediatric staff and of the operative reports from medical records with a review of the literature and medical records of patients with the condition was conducted.

Results: Two patients were successfully treated surgically.

Conclusion: Surgery is the treatment of choice for hemangioblastomas of the cervicomedullary junction. Careful monitoring for unique complications, treatment of the tumor as a vascular malformation, and screening for von Hippel Lindau must all be employed to safely care for this challenging group of patients.

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http://dx.doi.org/10.1007/s00381-006-0279-0DOI Listing

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