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Pioneering robotic-assisted Davydov vaginoplasty for Mayer-Rokitansky-Küster-Hauser syndrome.
BMJ Case Rep
January 2025
Obstetrics and Gynaecology, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India
Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome is a disorder marked by the congenital absence of the uterus and vagina. Patients with this condition often present with primary amenorrhoea and normal secondary sexual characteristics. The diagnosis of MRKH syndrome has profound implications for a patient's fertility and psychological well-being, necessitating a multidisciplinary approach that includes psychosocial support.
View Article and Find Full Text PDFMcIndoe Vaginoplasty in MRKHS: Case Report and Literature Review.
Clin Case Rep
December 2024
Department of Obstetrics and Gynecology Tribhuvan University, Institute of Medicine Kathmandu Nepal.
Mayer-Rokitansky-Küster-Hauser syndrome (MRKHS) is a rare congenital disorder characterized by agenesis of the uterus and upper two-thirds of the vagina. It affects around 1 in 4000-5000 females and is of two types: type 1, also known as isolated Müllerian aplasia or Rokitansky, which involves only uterovaginal agenesis, and type 2, presents as uterovaginal agenesis along with renal, cardiac, and other organ anomalies. Despite the absence of vaginal and uterine structures, individuals with MRKHS typically present with normal secondary sexual characteristics and ovarian functions.
View Article and Find Full Text PDFComplexities of complete androgen insensitivity syndrome: insights from a case report and literature review.
J Int Med Res
November 2024
Department of Gynecology, Faculty of Medicine, University Geomedi, Tbilisi, Georgia.
Article Synopsis
- Complete androgen insensitivity syndrome (CAIS) can lead to challenges in diagnosing individuals with a 46, XY karyotype who appear female due to their inability to respond to androgens.
- A case report details how a patient was misdiagnosed during surgery and later incorrectly identified as having another syndrome, but was ultimately given the correct diagnosis and a management plan that postponed surgery until after puberty.
- The report emphasizes the need for a multidisciplinary approach in managing CAIS, calling for improved awareness and personalized treatment plans to provide effective, patient-centered care.
MAYER-ROKITANSKY-KUSTER-HAUSER SYNDROME. LAPAROSCOPIC SIGMOID VAGINOPLASTY FOR THE TREATMENT OF VAGINAL AGENESIS - SINGLE CENTER EXPERIENCE IN GEORGIA. CASE REPORT.
Georgian Med News
September 2024
2Clinic Caraps Medline, Tbilisi, Georgia.
Introduction And Hypothesis: Sigmoid vaginoplasty is a safe and acceptable procedure for vaginal agenesis with good cosmetic results and acceptable complications rate. Sigmoid colon vaginoplasty is the treatment of choice because of its large lumen, thick walls resistant to trauma, adequate secretion allowing lubrication, not necessitating prolonged dilatation, and short recovery time. We investigate the feasibility, safety, and clinical therapeutic effect of laparoscopic sigmoid vaginoplasty in women with Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome.
View Article and Find Full Text PDFVariability in Design and Materials of Vaginal Stent or Moulds for Vaginal Agenesis - A Systematic Review.
J Hum Reprod Sci
September 2024
Shrimati Chandrawali Devi Dental Clinic, Rohtak, Haryana, India.
Background: Vaginal stents play a crucial role in both non-surgical and surgical management of vaginal agenesis. Different types of stents with variable designs and materials have been described in the literature. However, a summary of various stents described in the existing data and their outcome measures needs to be studied.
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