Low grade sarcoma of scrotal wall.

We report a rare case of low grade sarcoma of scrotal wall. A male child aged 2 1/2 years presented with history of scrotal lymphoedema involving the left side of scrotum, slowly progressive since birth. We planned scrotectomy but the patient was lost to follow-up. During intervening period, left inguinal omentopexy was done elsewhere. The patient again presented 3 years later with multiple swellings in scrotum. We performed almost complete scrotectomy with reconstruction of the scrotal defect using scrotal remnant as a stretchable musculocutaneous flap. A third of the residual scrotum could be expanded to resurface the entire scrotum. On histopathology, low grade malignant peripheral nerve sheath tumor of grade-I was confirmed. Post-operative follow-up showed no residual disease.