Malignant cylindroma of the external auditory canal.

Objective: This report describes a case of a malignant cylindroma arising in the external auditory canal.

Study Design: Retrospective surgical case review.

Setting: Tertiary care teaching hospital.

Intervention: Wide local excision with margin control.

Results: Local control of disease at 2-year follow-up.

Conclusion: To our knowledge, this is the first report describing a malignant degeneration of cylindroma in the external auditory canal. This tumor represents an extremely rare cutaneous neoplasm, thus raising diagnostic and therapeutic challenges.