Desmoplastic fibromas are rare bone tumors that have been reported in the adult skull but rarely in that of children. Although desmoplastic fibromas of the pediatric skull are uncommon, their similarity to benign skull lesions and their locally aggressive nature make them an important part of the differential diagnosis. Local recurrence is common after curettage alone but complete resection appears to be curative. Close follow up of incompletely resected lesions is essential. The authors detail three cases of pediatric desmoplastic fibromas of the skull and discuss diagnosis and treatment.
Download full-text PDF |
Source |
|---|---|
| http://dx.doi.org/10.3171/ped.2005.103.4.0362 | DOI Listing |
Publication Analysis
Top Keywords
Similar Publications
A Case of Desmoplastic Fibroma of the Thoracic Spine with Incomplete Paralysis of both Lower Limbs.
Spine Surg Relat Res
November 2024
Department of Orthopaedic Surgery, Shiga University of Medical Science, Shiga, Japan.
Airway management in pediatric patients undergoing microvascular free tissue transfer reconstruction after mandibulectomy.
Int J Pediatr Otorhinolaryngol
December 2024
Department of Otolaryngology-Head and Neck Surgery, Indiana University School of Medicine, Indianapolis, IN, USA. Electronic address:
Objectives: Microvascular free tissue transfer (MVFTT) for head and neck reconstruction is infrequently performed in pediatric patients. There is a paucity of data on perioperative airway management in pediatric MVFTT, such as the need for tracheostomy, which can pose higher morbidity to young patients due to potential long-term effects on the softer, more pliable laryngotracheal cartilage. Our objective was to report airway outcomes on pediatric patients undergoing MVFTT after segmental mandibulectomy with or without tracheostomy.
View Article and Find Full Text PDFDesmoplastic Fibroblastoma (Collagenous Fibroma) of the Knee: A Case Report and Literature Review.
Cancer Diagn Progn
November 2024
Section of Orthopaedic Surgery, Department of Medicine, Fukuoka Dental College, Fukuoka, Japan.
Background/aim: Desmoplastic fibroblastoma, also known as collagenous fibroma, is a rare benign mesenchymal neoplasm that primarily arises in the subcutaneous tissue of upper extremities and limb girdles. The knee is an uncommon location for desmoplastic fibroblastoma. Recent studies have demonstrated the presence of immunoreactivity for FOS like 1 (FOSL1) and rearrangements of FOSL1.
View Article and Find Full Text PDFDesmoplastic Fibroma of the Gnathic Bones-A Systematic Review.
Oral Dis
October 2024
Department of Stomatology, Porto Alegre Clinics Hospital (HCPA/UFRGS), Porto Alegre, Rio Grande do Sul, Brazil.
Article Synopsis
- The study aims to compile and summarize information about desmoplastic fibroma in the jaw bones, focusing on its key characteristics.
- A systematic review identified 66 articles detailing 96 cases, revealing a higher prevalence in females and younger patients, particularly affecting the mandible, with painless swelling as the primary symptom.
- Surgical removal is the standard treatment with a recurrence rate of 10.8%, and histopathological analysis shows specific cellular and molecular features that require more research for understanding the tumor's development.
Desmoplastic fibroma of the mandible in a 5-year-old child as an early oral manifestation of familial adenomatous polyposis.
Int J Oral Maxillofac Surg
December 2024
Department of Oral and Maxillofacial Surgery, Nair Hospital Dental College, Mumbai, Maharashtra, India; Department of Dentistry, B.J. Government Medical College and Sassoon General Hospital, Maharashtra, India.
Article Synopsis
- Desmoplastic fibroma (DF) is a rare, benign but locally aggressive tumor found in the mandible that often resembles other oral lesions.
- Familial adenomatous polyposis (FAP) leads to multiple colorectal polyps and has various oral manifestations, making it significant in the context of DF.
- A case study of a 5-year-old with DF showed no recurrence after surgery, and subsequent genetic testing identified FAP, highlighting the need for careful diagnosis and genetic screening in similar cases.
Want AI Summaries of new PubMed Abstracts delivered to your In-box?
Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!