AI Article Synopsis
- Dermatofibrosarcoma protuberans is a rare skin tumor with intermediate malignant potential, known for slow growth, local malignancy, and a high chance of recurrence.
- It represents about 0.1% to 0.18% of all malignant skin tumors, most commonly occurring in individuals aged 20 to 40 years.
- This study involved a retrospective analysis of 28 cases, focusing on the clinical features, histopathology, and immunohistochemistry of the tumor.
Article Abstract
Dermatofibrosarcoma protuberans of Darier and Ferrand is a mesenchymatous skin tumor of intermediate malignant potential, characterised by slow growth, local malignancy and a high rate of recurrence. It is a rare tumor, accounting for approximately 0.1% to 0.18% of all malignant skin tumors. Peak incidence of the disease is between 20 to 40 years of age. We report a retrospective study of 28 cases of dermatofibrosarcoma protuberans. We reviewed the clinical features, histopathological and immunohistochemical aspects of this tumor.
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