Spontaneous splenic rupture associated with hepatosplenic gammadelta T-cell lymphoma.

J Formos Med Assoc

Division of General Surgery, Department of Surgery, Tri-Service General Hospital, National Defense Medical Center, Taipei, Taiwan.

Published: August 2005

AI Article Synopsis

  • Spontaneous splenic rupture is a rare but serious issue that can occur in patients with hematologic cancers, despite the spleen commonly being affected in these conditions.
  • A case was presented involving a 50-year-old healthy man who experienced sudden symptoms leading to a ruptured spleen, necessitating emergency surgery.
  • The findings indicated he had hepatosplenic gammadelta T-cell lymphoma, a type of cancer not specifically classified by the World Health Organization.

Article Abstract

Spontaneous splenic rupture is an uncommon but life-threatening complication of hematologic malignancies, despite the frequent involvement of the spleen in these diseases. It has been reported in patients with acute and chronic leukemia, Hodgkin's disease, non-Hodgkin's lymphoma, and histiocytic lymphoma. A 50-year-old previously healthy man presented with acute symptoms of spontaneous splenic rupture. Emergency splenectomy with liver biopsy was performed. The clinicopathologic features suggested a hepatosplenic gammadelta T-cell lymphoma (HSgammadeltaTL). Here, we report a rare case of spontaneous splenic rupture associated with HSgammadeltaTL, unspecified in the World Health Organization classification.

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