A cardiac paraganglioma presenting with atypical chest pain.

Eur J Cardiothorac Surg

Cardiothoracic Division, The James Cook University Hospital, Marton Road, Middlesbrough TS4 3BW, UK.

Published: August 2005

AI Article Synopsis

  • Primary cardiac tumors are rare, with the majority being benign and 75% classified as atrial myxomas; however, cardiac paragangliomas are also notable benign tumors.
  • A case study of a 56-year-old male revealed a large vascular mass on the intra-atrial septum after he experienced chest pain, arm tingling, and breathing difficulties.
  • Despite normal test results for tumors and hormones, the tumor's extensive involvement made complete removal impossible, leading to a novel approach of ligating feeding vessels, which successfully stabilized the patient over two years.

Article Abstract

Primary cardiac tumours are rare. The majority are benign and 75% are atrial myxomas. One of the more unusual benign tumours affecting the heart is a cardiac paraganglioma. A 56-year male was presented with a 6-month history of vague, left-sided chest pain, intermittent parathesia of the left arm and dyspnoea on bending. Echocardiography documented a large, highly vascular mass, attached to the intra-atrial septum. All investigations, haematological, biochemical, neuroendocrine tumour markers and urinary cathecholamine levels, were within normal limits. Macroscopically the tumour involved the whole of the atrial septum, roof of the left atrium and extended to surround the superior vena cava, excluding total resection. The feeding vessels were ligated in the hope of infarcting the remainder of the tumour. In over 2-years of follow-up, the patient remains clinically stable. To our knowledge this is the first reported case where vascular ligation has been used to control a cardiac paraganglioma.

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http://dx.doi.org/10.1016/j.ejcts.2005.04.038DOI Listing

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