Pheochromocytoma is a neoplasia of chromaffin cells that is very rare in children. Its signs and symptoms result from the release of catecholamines. We report the case of a child with pheochromocytoma of difficult clinical management, confirmed on the anatomicopathological study, and cured after surgical resection.
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Article Synopsis
- Phaeochromocytoma and paraganglioma (PPGL) are rare tumors that develop from specialized cells in the adrenal gland or nearby nerve tissues, affecting both adults and, less commonly, children.
- The annual incidence in children is approximately 0.5 cases per million, and there's been significant progress in understanding how to diagnose and treat these tumors, primarily based on adult studies.
- This article reviews the unique challenges and management strategies for diagnosing and treating pediatric PPGL, including recent international guidelines.
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