A case of arrhythmogenic right ventricular dysplasia (ARVD) in a 28 year old man is reported. Diagnosis was based on ECG, echocardiographic and scintigraphic findings. Echocardiography and scintigraphy revealed an enlarged right ventricle and normal left ventricle. The abnormalities specific for ARVD were free wall motion abnormalities, particularly akinetic areas and microaneurysms . Ventricular tachycardia and premature ventricular contractions of left bundle branch block (LBBB) pattern were recorded. A titer against mycoplasma and concentrations of immunoglobulins were normal. Anti-++ smooth muscle antibodies were detected. The patient was treated with amiodarone . There were no clinical, echocardiographic and ECG features of ARVD in the patient's brother.
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