Hemangiopericytomas are rare soft-tissue neoplastic lesions that can arise in any part of the body. They are mesenchymal tumors that account for 3 to 5% of all soft-tissue sarcomas and 1% of all vascular tumors. They originate in extravascular cells (pericytes). Some 15 to 30% of all hemangiopericytomas occur in the head and neck; of these, approximately 5% occur in the sinonasal area. We describe our brief retrospective review of 7 histologically proven cases of sinonasal hemangiopericytoma, and we discuss the imaging characteristics and clinical and pathologic findings in these patients.
Download full-text PDF |
Source |
|---|
Publication Analysis
Top Keywords
Similar Publications
Uncommon Nasal Mass Presentation: A Radiological Case Series.
J Pers Med
December 2024
Radiological Sciences Section, Department of Biomedicine, Neuroscience and Advanced Diagnostics, University of Palermo, AOUP "Paolo Giaccone", Via del Vespro 129, 90127 Palermo, Italy.
Nasal and paranasal sinus masses can arise from a wide range of conditions, both benign and malignant, as well as congenital or acquired. Diagnosing these masses is often challenging, requiring a combination of nasal endoscopy, imaging studies, and histopathological analysis. Initial imaging frequently involves computed tomography or cone beam computed tomography (CBCT) to evaluate the bony anatomy of the nasal cavity and surrounding sinuses, while magnetic resonance imaging (MRI) is typically used for detailed assessment of soft tissues and to aid in differential diagnosis when the findings are inconclusive.
View Article and Find Full Text PDFSpindle Cell Neoplasms Unique to the Sinonasal Tract.
Surg Pathol Clin
December 2024
Department of Pathology, Microbiology & Immunology, Vanderbilt University Medical Center, 445 Great Circle Road, Office 1959, Nashville, TN 37228, USA.
Article Synopsis
- - The spindle cell neoplasms encompass three main types: sinonasal tract angiofibroma (STA), glomangiopericytoma (GPC), and biphenotypic sinonasal sarcoma (BSNS), which share similarities in their clinical and biological features.
- - Sinonasal tract angiofibroma (STA) is characterized by a collagen-rich, vascular stroma often linked to hormonal changes.
- - Glomangiopericytoma (GPC) has a distinct appearance with a consistent ovular shape and shows Beta-catenin accumulation, while biphenotypic sinonasal sarcoma (BSNS) displays characteristics resembling neural tissue and co-expresses S100 and smooth muscle markers along with
Head and Neck Myopericytoma (MPC): A Case Report of Double Synchronous Sinonasal MPC.
Ann Ital Chir
October 2024
Department of Otolaryngology-Head and Neck Surgery, IEO-European Institute of Oncology IRCCS, 20141 Milan, Italy.
Aim: Myopericytoma (MPC) is a rare tumour characterized by a perivascular proliferation of pericytic cells with myoid differentiation and a typical spindle shape. Except for the rare malignant cases, MPC mostly shows a benign course. Symptoms are often non-specific, and the diagnosis could be accidental.
View Article and Find Full Text PDFTumour masquerading juvenile angiofibroma in a female; unveiling glomangiopericytoma-a rare sinonasal histopathology.
BMJ Case Rep
August 2024
ENT, Jawaharlal Institute of Postgraduate Medical Education and Research, Puducherry, India.
Sinonasal tumours of varying histology are not unusual in otolaryngology surgical practice. Juvenile angiofibroma (JAs) are vascular tumours usually occurring in adolescent male population; but rare in females. But similar clinical and radiological presentations are possible in females inducing strong suspicion of JA which needs to be ruled out by detailed evaluation.
View Article and Find Full Text PDFBreaking New Ground: Unraveling Sinonasal Hemangiopericytoma Through a Rare Case Series on Endoscopic Excision and Postoperative Monitoring.
Indian J Otolaryngol Head Neck Surg
August 2024
NRG Oncology/Hillman Cancer Center, NSABP Foundation, Inc., 1307 Federal St, Suite 303, Pittsburgh, PA 15212 USA.
Hemangiopericytoma is a rare vascular neoplasm derived from pericytes, with uncertain malignant potential. It mainly occurs in the retroperitoneum and lower extremities, with a lower incidence in the head and neck region and nasal cavity. Diagnosis is aided by histopathological examination and immunohistochemistry.
View Article and Find Full Text PDFWant AI Summaries of new PubMed Abstracts delivered to your In-box?
Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!