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Unilateral Facial Swelling in a Sickle Cell Patient.
Cureus
August 2024
Pediatric Emergency Medicine, Children's Mercy Hospital, Kansas City, USA.
Acute soft head syndrome (ASHS) is a rare complication of sickle cell disease that often requires a high index of suspicion and is often a diagnosis of exclusion. We present the case of an 18-year-old male with sickle cell disease in the United States who developed acute soft head syndrome without known traumatic injury. The goal of this case presentation is to provide awareness and education regarding a rare complication of sickle cell disease and recommended management for the associated symptoms.
View Article and Find Full Text PDFBeta-Thalassemia Presenting as Moyamoya Syndrome With a Review of Skeletal Manifestations.
Cureus
May 2023
Department of Radiology, Osmania Medical College, Hyderabad, IND.
Moyamoya angiopathy (MMA) is a progressive vasculopathy characterized by slowly progressive stenosis involving the proximal portions of the major intracranial arteries, resulting in strokes and intracranial hemorrhages. If it occurs secondary to a known cause, it is called Moyamoya syndrome (MMS). Here, we describe the case of a five-year-old male child who presented to us with symptoms of stroke and, upon evaluation, revealed Moyamoya angiopathy.
View Article and Find Full Text PDFAn atypical imaging characteristic of calvarial metastasis of neuroblastoma as multiple multi-loculated cystic masses with internal blood-fluid levels: a case report.
BMC Neurol
December 2022
Department of Radiology, Children's Medical Center of Excellence and Dr. Shariati Hospital, Tehran University of Medical Sciences, Tehran, Iran.
Background: As the third most common malignancy of childhood, Neuroblastoma has a great propensity to metastasize to multiple organs. The most common site of metastasis is the bone and bone marrow. Concerning the central nervous system, neuroblastoma usually involves the calvarium and the external dural surface.
View Article and Find Full Text PDFHair-on-End Sign in a 9-Year-Old Girl Presenting with Acute Stroke in Sickle Cell Disease.
Int Med Case Rep J
February 2022
Department of Radiology, Mbarara University of Science and Technology, Mbarara City, South-Western Uganda, Uganda.
Background: The hair-on-end (HOE) sign is a rare finding seen in the diploic space on skull radiographs, computed tomography (CT) and magnetic resonance imaging (MRI) with the appearance of long, thin vertical striations of calcified spicules perpendicular to the bone surface that looks like hair standing on end. It is classically seen in children/adolescents with hemolytic anemias, in particular, thalassemia major and sickle cell disease. Here, we present a 9-year-old Ugandan girl who presented with stroke in whom head CT demonstrated cerebral intraparenchymal hemorrhage and multiple infarcts on the left with HOE sign.
View Article and Find Full Text PDFGross and radiographic appearance of porotic hyperostosis and cribra orbitalia in thalassemia affected skulls.
Anat Cell Biol
June 2021
Department of Anatomy, Faculty of Medicine, Khon Kaen University, Khon Kaen, Thailand.
Porotic hyperostosis (PH) is the expansion of the cranial diploë, generating 'hair-on-end' appearance on X-rays. This condition is extremely rare and had a prevalence of 0.08%.
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