[Ureteropelvic stenosis, agenesia of the contralateral kidney and sinistral inferior vena cava].

Introduction: Ureteropelvic stenosis occurs as a result of intraluminal or extraluminal alterations at the ureteropelvic junction. It is the most common cause of upper urinary tract obstruction.

Case Report: We report about a rare case of a man with ureteropelvic junction obstruction and a renal pelvic stone accompanied by other congenital anomalies, including a sinistral inferior vena cava and agenesis of the opposite kidney. Multiple vessels were present in front of the renal pelvis, while the renal vein itself was situated dorsal to the left renal pelvis, resulting in compression and obstruction of the ureteropelvic junction. Dismembered pyeloplasty using the Anderson-Hynes technique was performed placing the ureter dorsal to the renal vein.

Conclusion: Various vascular anomalies, especially in the region of the vena cava, can result in renal vasculature abnormalities and development of secondary ureteropelvic stenosis. Ureteropelvic stenosis may coexist with other congenital defects.