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Similar Publications

Sturge Weber Syndrome--unusual presentation.

J Ayub Med Coll Abbottabad

December 2014

Sturge Weber Syndrome or encephalo-trigeminal angiomatosis is non-hereditary, congenital and rare disorder of unknown aetiology. It is characterised by vascular malformation with capillary venous angiomas involving face, eye and leptomeninges resulting in neurological and orbital manifestations. A case of 23 years old female presented with history of tonic-clonic convulsions, evidence of Port wine stain on face since birth, characteristic CT findings diagnosed as a case of Sturge Weber Syndrome is reported here for its rarity.

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A case report of rare congenital disease of encephalo-trigeminal angiomatosis (Sturge-Weber Syndrome) (SWS), is presented to alert the anesthesiologist of its potential risk. The case was anesthetized for emergency orthopedic surgery. Anesthesia management is directed towards observing the clinical manifestations of localized superficial skin lesions, extensive systemic involvement, evaluating its associated anomalies and anticipating difficult intubation due to angiomas of the mouth and upper airway and be a ware of concurrent therapy.

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Sturge Weber syndrome.

Indian J Dent Res

August 2005

Department of Oral Pathology and Microbiology, College of Dental Surgery, Kasturba Medical College, Mangalore.

A variant of hemangioma and an uncommon congenital condition, the Sturge Weber syndrome (SWS), also called encephalo trigeminal angiomatosis, is a neurocutaneous disorder with angiomas involving the skin of the face (cutaneous angioma) and pia arachnoid (leptomeningeal angioma). It occurs typically in the ophthalmic and maxillary distributions of the trigeminal nerve (1,2). Here we present a case of a 14 year old girl.

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[Sturge-Weber-Krabbe syndrome (or encephalo-trigeminal angiomatosis)].

Ann Dermatol Venereol

April 2004

Service de Dermatologie, Département Peau et Morphologie, CHU, 37044 Tours Cedex 01.

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A study of 9 cases of trigeminal noevus flammeus was performed. Eight had congenital glaucoma and where followed from 1 to 10 years. Only three had intracranial involvement.

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