AI Article Synopsis
- Sotos syndrome is an overgrowth disorder linked to a high rate of congenital heart defects, with 6 out of 60 patients in the study having these issues.
- The case discusses a successful heart surgery, total cavopulmonary connection, performed on a 30-month-old patient with specific heart defects, including pulmonary atresia.
- The patient's recovery after the operation went smoothly, with no complications reported.
Article Abstract
Sotos syndrome is an overgrowth disorder of unknown etiology associated with a high incidence of congenital heart defects. Of 60 patients with Sotos syndrome treated in our hospital, 6 had congenital heart defects. We describe a case of successful total cavopulmonary connection at 30 months of age in a patient having pulmonary atresia with intact ventricular septum and a patent ductus arteriosus who had walking disability. The postoperative course was uneventful.
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| http://dx.doi.org/10.1177/021849230301100415 | DOI Listing |
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