A vulvar carcinoma is a malignant disease concerning women usually in their 7th or 8th decade of life. The course of this disease is very dynamic in young females. It is often diagnosed in the advanced stage, when it should be treated as a systemic disease. We present a case which is an example of a very sudden course, the diagnostic difficulty and the evidence of the systemic process of the disease. The case is a challenge to make an attempt to apply combined treatment in such cases.
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