AI Article Synopsis

  • A patient with Crohn's disease exhibited an unusual case of Wegener's granulomatosis, presenting with facial ulcers and 7th cranial nerve palsy.
  • Wegener's granulomatosis typically affects the lungs, kidneys, and eyes, but skin involvement occurs in about half of the cases and can be an initial sign in 9-14% of patients.
  • Timely and accurate diagnosis is crucial because Wegener's granulomatosis can be life-threatening if left untreated.

Article Abstract

We report a case of an unusual presentation of Wegener's granulomatosis (WG) in a patient with Crohn's disease (CD). She presented to our Wound Care Center with 7th cranial nerve palsy and facial pyoderma-like ulcerations. Although WG has a predilection for the lung, kidney, and eyes, cutaneous involvement can be seen in 50% of the cases, and it can be the presenting sign in 9-14%. Because of the lethality of WG if not properly treated, the diagnosis is imperative.

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http://dx.doi.org/10.1046/j.1365-4362.2003.01919.xDOI Listing

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