[Primary intracranial Ewing's sarcoma of the mastoid bone. A case report].

Introduction: Ewing s sarcoma (ES) is a tumorous process that is found mainly in long bones and the pelvis, but its primary location is not often the intracranial zone.

Case Report: We report the case of a 5 year old patient who visited surgery 30 days before hospital admission with increased volume of the left mastoid bone, torticollis, balance disorders and discoordinated movements. A computerised tomography brain scan confirmed our suspicions of a tumorous lesion that was destroying the left mastoid bone, and was invading the projection of the left hemispherium cerebri and edges of the brain stem (mid brain). The patient was submitted to surgery and a partial excision was performed. A month later, another operation was carried out and the patient died after several days in the intensive care unit from serious respiratory complications.

Conclusions: The tumour marker CD 99 is specifically used to diagnose ES. We think that, when faced with a patient suffering from ES, conduct must always be aggressive, with early surgery and, later, adjuvant therapy.