AI Article Synopsis
- A 31-year-old female with Ehlers-Danlos syndrome type IV experienced simultaneous bilateral renal artery dissection and a hematoma in the ascending aorta.
- She had previously delivered without complications six months prior and was found to have situs solitus with dextrocardia.
- Despite conservative management of her complications, she succumbed to a pulmonary infection and multi-organ failure shortly after admission.
Article Abstract
A report is presented of a 31 year female patient with Ehlers-Danlos syndrome type IV who presented a bilateral renal artery dissection and a hematoma of the ascending aorta simultaneously. She had had an uneventful delivery six months before. We also discovered a situs solitus with dextrocardia in this patient. These complications were managed conservatively. Unfortunately the patient died of a pulmonary infection and a multi-organ failure syndrome several days after her admission.
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| http://dx.doi.org/10.1016/s0967-2109(02)00079-0 | DOI Listing |
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