Noncompaction of the ventricular myocardium sometimes referred to as spongy myocardium, is a rare congenital cardiomyopathy resulting from an arrest in normal endomyocardial embryogenesis. The characteristic echocardiographic findings of this disease consist of multiple myocardial trabeculations and deep intertrabecular recesses communicating with the left ventricular cavity. Familial occurrence has been observed. We present an illustrative case of isolated noncompaction of the ventricular myocardium in a 16-year-old patient, with the typical clinical and echocardiographic features of the disease. The literature on the topic is reviewed.
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