Dynamic thoracoplasty for asphyxiating thoracic dystrophy.

Ann Thorac Surg

Department of Surgery, American University Medical Center, Beirut, Lebanon.

Published: November 2001

The life-saving procedures to expand the chests of infants born with Jeune asphyxiating thoracic dystrophy provide a static solution incapable of responding to the growth demands of thriving patients. We describe an instrument that provided a dynamic solution for an infant, where an initial methyl methacrylate midsternotomy spacer placed at 4 months of age was followed at 11 months with recurrence of his difficulties. At 8 months after the second operation the patient was stable and thriving with no recurrence of symptoms. The instrument modifications, limitations, and possible complications are described.

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http://dx.doi.org/10.1016/s0003-4975(01)02565-6DOI Listing

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