Caudal Regression Syndrome and peno-scrotal transposition.

Saudi Med J

Department of Pediatric Surgery, Al-Noor Specialist Hospital, Makkah-Al-Mukarrama, Kingdom of Saudi Arabia.

Published: June 2001

Caudal Regression Syndrome is a rare anomaly affecting different systems in the caudal portion of the fetus. Peno-scrotal transposition is a rare condition of variable severity often associated with Caudal Regression Syndrome. We report a case of Caudal Regression Syndrome with perineal ano-rectal duplication, incomplete peno-scrotal transposition, perineal hypospadias, chordee, and thoracic hemivertebrae.

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