Idiopathic retroperitoneal fibrosis is a rare disease and a delay in diagnosis may cause renal failure. Medical treatment i.e. corticotherapy or more recently, tamoxifene has been used successfully. This approach is recommended in patients either with moderate obstruction of the upper urinary, risk of major surgery or in cases of recurrence after surgical treatment. Ureterolysis using conventional surgery or laparoscopy remains the treatment of choice. This procedure should be considered in patients with neoplasic fibrosis, corticoresistant fibrosis or in cases of peri-aneurysm fibrosis.
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http://dx.doi.org/10.1016/s0003-4401(01)00017-1 | DOI Listing |
Zhongguo Yi Xue Ke Xue Yuan Xue Bao
February 2025
Department of Radiology, Fushun Central Hospital,Fushun,Liaoning 113006,China.
Objective To analyze the value of abdominal CT images combined with serological indicators in predicting the ureteral involvement in idiopathic retroperitoneal fibrosis(IRF). Methods The CT images of 79 IRF patients were analyzed retrospectively,including the involved sites and enhancement characteristics of the lesions.According to the inclusion and exclusion criteria,43 patients with complete serological data were selected and assigned into a ureteral involvement group(=29)and a non-ureteral involvement group(=14) according to whether ureters were involved in IRF.
View Article and Find Full Text PDFInt J Surg Case Rep
March 2025
Kilimanjaro Christian Medical Centre (KCMC), Box 3010, Moshi, Tanzania; Kilimanjaro Medical University College (KCMUCo), Box 2240, Moshi, Tanzania; Department of General Surgery, Kilimanjaro Christian Medical Center, Box 3010, Moshi, Kilimanjaro, Tanzania.
Background: Retroperitoneal cysts are rare, accounting for less than 1% of retroperitoneal tumors. Idiopathic giant unilocular retroperitoneal cysts are even more uncommon, with very few reported cases. Their diagnosis and management are particularly challenging in resource-limited settings due to restricted access to advanced imaging and surgical techniques.
View Article and Find Full Text PDFIntern Emerg Med
March 2025
Rheumatology Division, University Hospital Marqués de Valdecilla, IDIVAL, Immunopathology Group, Santander, Spain.
Aortitis and periaortitis refer to the inflammation of the aortic wall and the surrounding tissues. Both conditions are associated with various diseases and express nonspecific manifestations. Early diagnosis and treatment are crucial to improve the prognosis of the disease.
View Article and Find Full Text PDFAbdom Radiol (NY)
March 2025
Department of Radiology and Biomedical Imaging, Yale School of Medicine, New Haven, USA.
Retroperitoneal fibrosis (RPF) is a rare fibroinflammatory disease with idiopathic and secondary causes. Idiopathic disease is more common and is believed to be immune mediated; associations with autoimmune diseases and/or inflammatory disorders such as IgG4 related disease are often present. Common complications include hydronephrosis and venous stenosis and/or thrombosis.
View Article and Find Full Text PDFPrague Med Rep
March 2025
Department of Clinical and Experimental Pathology, IKEM, Prague, Czech Republic.
Ormond's disease is a systemic autoimmune disease with serious complications. We present our retrospective analysis of 83 patients diagnosed with and treated for idiopathic retroperitoneal fibrosis (Ormond's disease) in our department from 1997 to 2023. In this retrospective study, we analysed the diagnostic approaches, the clinical history and surgical and immunosuppressive therapies, and their subsequent effects on our patients.
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