Wilson's disease.

Clin Liver Dis

Department of Medicine, Albert Einstein College of Medicine, Yeshiva University, Bronx, New York, USA.

Published: February 2000

During the last 90 years, Wilson's hepatolenticular degeneration has evolved from a disease presenting insurmountable challenges to the clinician's diagnostic acumen to a metabolic disorder which is diagnosable woth certainty, treatable successfully, and even preventable. It may be long before the genetic defect becomes amenable to correction and a cure of the disease becomes possible.

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http://dx.doi.org/10.1016/s1089-3261(05)70105-7DOI Listing

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