Waldman disease, also called intestinal lymphangiectasis, is a protein-loosing enteropathy caused by anomalous intestinal lymphatic canals. The condition is transmitted by autosomal dominant inheritance. Diet therapy including medium chain triglycerides improves the disease course. The condition occurs in early childhood. We report a case observed in a pregnant woman with intestinal lymphangiectasis. She delivered a full-term infant and experienced no major complications.
Download full-text PDF |
Source |
|---|
Publication Analysis
Top Keywords
Similar Publications
Case 332: Tyrosine Kinase Inhibitor-induced Intestinal Lymphangiectasia.
Radiology
December 2024
From the Department of Radiology, Mayo Clinic Arizona, 5777 E Mayo Blvd, Phoenix, AZ 85054.
History A 65-year-old male patient with a history of sarcomatoid renal cell carcinoma and prior right nephrectomy developed recurrent disease adjacent to the inferior vena cava. The patient underwent surveillance imaging 7 months after initiation of treatment with maximum-dose pazopanib and less than 1 month after completing a 2-month regimen of palliative stereotactic body radiation therapy to the right nephrectomy bed and site of recurrence. (Stereotactic body radiation therapy was initiated 5 months after pazopanib treatment was initiated.
View Article and Find Full Text PDF[Clinical features of 50 patients with primary intestinal lymphangiectasia].
Zhonghua Wai Ke Za Zhi
December 2024
Department of Lymphatic Surgery, Beijing Shijitan Hospital, Capital Medical University, Beijing100038, China.
To investigate the clinical features of primary intestinal lymphangiectasia (PIL). This study was a retrospective case series study. Fifty consecutive patients diagnosed with PIL in Department of Lymphatic Surgery, Beijing Shijitan Hospital, Capital Medical University from March 2019 to March 2021 were included and their clinical data was retrospectively reviewed.
View Article and Find Full Text PDFClinical assessment of small bowel capsule endoscopy in pediatric patients.
Front Med (Lausanne)
October 2024
Department of Gastroenterology, Ministry of Education Key Laboratory of Child Development and Disorders, China International Science and Technology Cooperation Base of Child Development and Critical Disorders, Chongqing Key Laboratory of Pediatrics, National Clinical Research Center for Child Health and Disorders, Children's Hospital of Chongqing Medical University, Chongqing, China.
Introduction: Small bowel capsule endoscopy is a first-line examination method for small bowel diseases, which can find small intestinal lumen and mucosal lesions.
Methods: We retrospectively assessed patients who underwent small bowel capsule endoscopy between September 2020 and May 2023 to examine their clinical and small bowel capsule endoscopic data, aiming to provide insights into the application of this technique in pediatric patients with small intestinal diseases.
Results: All instances of capsule retention were successfully resolved through enteroscopy.
First case report of intestinal lymphangiectasia with refractory bleeding from the duodenum, successfully treated by intra-abdominal lymphaticovenous anastomosis with venous ligation.
Clin J Gastroenterol
October 2024
Department of Gastroenterology, Graduate School of Medicine, The University of Tokyo, Hongo 7-3-1, Bunkyo-Ku, Tokyo, 113-8655, Japan.
Article Synopsis
- Intestinal lymphangiectasia (IL) is a condition that causes a loss of protein from the digestive system, which can sometimes lead to gastrointestinal bleeding.
- A 41-year-old woman with a long history of this condition experienced worsening symptoms despite various treatments and became dependent on blood transfusions.
- After undergoing a surgical procedure to address the leakage of lymph fluid into her digestive tract, she saw significant improvement and remained symptom-free for over six months.
Primary intestinal lymphangiectasia: A case report.
J Pediatr Gastroenterol Nutr
May 2024
Service de Dermatologie, CHU, Inserm 1098, Besançon, France.
Want AI Summaries of new PubMed Abstracts delivered to your In-box?
Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!