Introduction: The combination of a horseshoe kidney with a retrocaval ureter in one patient is extremely rare.
Presentation Of Case: A 12-year-old adolescent presented with the compliant of absent testis in the right scrotum since birth with incidental radiologic finding of horseshoe kidney with retrocaval ureter.
Clinical Findings And Investigations: Physical examination was unremarkable except for a left non-palpable testis.