Rationale: Individuals diagnosed with neurofibromatosis type I (NF1) commonly present with neurofibromas, and a subset may progress to develop malignant peripheral nerve sheath tumors (MPNST) during their lifetime. Diagnosing and treating MPNST, typically linked to NF1, poses challenges for clinicians due to its histopathological complexity.
Patient Concerns: A 25-year-old male presented with postprandial discomfort and vomiting, subsequently developing left mid-abdominal pain.