[Analysis of a Chinese pedigree affected with Spinal muscular atrophy due to compound heterozygous variants of SMN gene].

Objective: To analyze variants of SMN gene in a Chinese pedigree affected with Spinal muscular atrophy (SMA).

Methods: A Chinese pedigree diagnosed at the Nanchang First Hospital in January 2020 was selected as the study subject. Peripheral blood samples were collected for the extraction of DNA.

Theoretical, thermodynamic and electrochemical analysis of biotin drug as an impending corrosion inhibitor for mild steel in 15% hydrochloric acid.

The corrosion mitigation efficiency of biotin drug for mild steel in 15% hydrochloric acid was thoroughly investigated by weight loss and electrochemical methods. The surface morphology was studied by the contact angle, scanning electrochemical microscopy, atomic force microscopy and scanning electron microscopy methods. Quantum chemical calculation and Fukui analysis were done to correlate the experimental and theoretical data.

Heterocyclic Corrosion Inhibitors for J55 Steel in a Sweet Corrosive Medium.

The inhibitory effect of two heterocyclic porphyrin compounds, specifically 5,10,15,20-tetrakis(pentafluorophenyl)-21,23-porphyrin palladium(II) (PF-1) and 4,4',4″,4‴-(porphyrin-5,10,15,20-tetrayl)tetrakis(benzoic acid) (PF-2), was studied in a sweet corrosion environment (3.5 wt % NaCl + CO) on J55 steel by means of weight loss and electrochemical methods. Surface changes were studied using contact angle, scanning electrochemical microscopy (SECM), and atomic force microscopy (AFM) techniques.

An impending inhibitor useful for the oil and gas production industry: Weight loss, electrochemical, surface and quantum chemical calculation.

The influence of a Schiff base namely N,N'-(pyridine-2,6-diyl)bis(1-(4-methoxyphenyl) methanimine) (PM) on the corrosion of J55 and N80 steel in 3.5 wt.% NaCl solution saturated with CO was evaluated using weight loss, potentiodynamic polarization, electrochemical impedance spectroscopy (EIS), X-ray diffraction (XRD), contact angle, scanning electron microscopy (SEM), atomic force microscopy (AFM) and scanning electrochemical microscopy (SECM).

Cluster statistics and quasisoliton dynamics in microscopic optimal-velocity models.

Using the non-linear optimal velocity models as an example, we show that there exists an emergent intrinsic scale that characterizes the interaction strength between multiple clusters appearing in the solutions of such models. The interaction characterizes the dynamics of the localized quasisoliton structures given by the time derivative of the headways, and the intrinsic scale is analogous to the "charge" of the quasisolitons, leading to non-trivial cluster statistics from the random perturbations to the initial steady states of uniform headways. The cluster statistics depend both on the quasisoliton charge and the density of the traffic.

A Dynamic Health Assessment Approach for Shearer Based on Artificial Immune Algorithm.

In order to accurately identify the dynamic health of shearer, reducing operating trouble and production accident of shearer and improving coal production efficiency further, a dynamic health assessment approach for shearer based on artificial immune algorithm was proposed. The key technologies such as system framework, selecting the indicators for shearer dynamic health assessment, and health assessment model were provided, and the flowchart of the proposed approach was designed. A simulation example, with an accuracy of 96%, based on the collected data from industrial production scene was provided.