Factors associated with right ventricular dilatation and dysfunction in patients with chronic pulmonary regurgitation after repair of tetralogy of Fallot: analysis of magnetic resonance imaging data from 218 patients.

Objective: The aim of the present study was to identify the factors associated with right ventricular (RV) dilatation and dysfunction in patients with chronic pulmonary regurgitation (PR) after repair of tetralogy of Fallot.

Methods: From April 2002 to June 2013, 218 patients with repaired tetralogy of Fallot underwent magnetic resonance imaging; 165 (76%) underwent transannular repair and 36 (17%) underwent nontransannular repair. Linear regression analyses were used to identify the predictors for RV end-diastolic volume index (EDVI), end-systolic volume index (ESVI), and ejection fraction.

Does limited right ventriculotomy prevent right ventricular dilatation and dysfunction in patients who undergo transannular repair of tetralogy of Fallot? Matched comparison of magnetic resonance imaging parameters with conventional right ventriculotomy long-term after repair.

Objective: The objective of this study was to test the hypothesis that limited (<1 cm) right ventriculotomy (RV-tomy) in the setting of transannular tetralogy of Fallot (TOF) repair might result in less right ventricular (RV) dilatation and dysfunction compared with conventional RV-tomy.

Methods: Between June 2002 and April 2012, 113 patients with transannular repair of TOF underwent magnetic resonance imaging (MRI). Patients were divided into a limited RV-tomy group (n = 39) and a conventional RV-tomy group (n = 74).

The results of cardiopulmonary exercise test in healthy Korean children and adolescents: single center study.

Purpose: The cardiopulmonary exercise test (CPET) is an important clinical tool for evaluating exercise capacity and is frequently used to evaluate chronic conditions including congenital heart disease. However, data on the normal CPET values for Korean children and adolescents are lacking. The aim of this study was to provide reference data for CPET variables in children and adolescents.

Transcatheter closure of secundum atrial septal defect in patients over 60 years old.

Background And Objectives: Atrial septal defect (ASD) is the one of most common congenital heart diseases detected in adults. Along with remarkable development of device technology, the first treatment strategy of secundum ASD has been transcatheter closure in feasible cases. However, there are only a few publications regarding the results of transcatheter closure of ASD in elderly patients, especially those over 60 years of age.

Outcomes of pulmonary valve replacement in 170 patients with chronic pulmonary regurgitation after relief of right ventricular outflow tract obstruction: implications for optimal timing of pulmonary valve replacement.

Objectives: The objectives of this study were to evaluate outcomes of pulmonary valve replacement (PVR) in patients with chronic pulmonary regurgitation (PR) and to better define the optimal timing of PVR.

Background: Although PVR is effective in reducing right ventricular (RV) volume overload in patients with chronic PR, the optimal timing of PVR is not well defined.

Methods: A total of 170 patients who underwent PVR between January 1998 and March 2011 for chronic PR were retrospectively analyzed.

Bicuspid pulmonary valve implantation using polytetrafluoroethylene membrane: early results and assessment of the valve function by magnetic resonance imaging.

Objectives: The durability of bioprosthetic valves in the pulmonary position is suboptimal. The objectives of this study were to evaluate the early results of polytetrafluoroethylene (PTFE) bicuspid pulmonary valve (PV) implantation and to better define the function of this valve by magnetic resonance imaging (MRI).

Methods: Fifty-six patients who underwent PTFE bicuspid PV implantation between June 2009 and August 2011 were retrospectively analysed.

Durability of bioprosthetic valves in the pulmonary position: long-term follow-up of 181 implants in patients with congenital heart disease.

Objectives: Durability of bioprosthetic valves in the pulmonary position is not well defined. We examined the durability of bioprosthetic valves in the pulmonary position and risk factors associated with bioprosthetic pulmonary valve failure.

Methods: Between 1993 and 2004, 181 patients underwent pulmonary valve replacement using bioprostheses.

Early surgical correction of atrioventricular valvular regurgitation in single-ventricle patients.

Background: The purpose of this study is to evaluate the effectiveness of early surgical correction for atrioventricular valve regurgitation (AVVR) in single-ventricle patients.

Methods: The medical records of 39 single-ventricle patients who underwent atrioventricular surgery more than once between 1996 and 2008 were reviewed.

Results: The mean preoperative grade of AVVR was 2.

Long-term results after mitral valve repair in children.

Objective: We analysed the long-term results of mitral valve (MV) repair in children.

Methods: We reviewed clinical records of 139 children (<18 years) who underwent MV repair between 1988 and 2007. Patients with atrioventricular septal defect, single ventricle or atrioventricular discordance were excluded.

Midterm follow-up of the status of Gore-Tex graft after extracardiac conduit Fontan procedure.

Objective: Extracardiac conduit Fontan procedure has some theoretical advantages over other types of Fontan procedures, such as optimized flow dynamics, a lower frequency of arrhythmias, and technical ease of procedure. However, lack of growth potential and thrombogenicity of the artificial conduit is the main concern and can possibly lead to reoperation for the conduit stenosis. In this study, we investigated the change and the status of the Gore-Tex graft used in extracardiac conduit Fontan procedure.

Aorta to right atrial fistula following transcatheter closure of an atrial septal defect.

The percutaneous transcatheter closure of atrial septal defects (ASDs) has become an acceptable alternative to surgical repair. The investigators present a case of aorta-to-right atrial fistula after the closure of an ASD using the Amplatzer septal occluder (ASO). After the surgical removal of the ASO, the ASD patch closure, and the repair of the fistula, the patient eventually recovered.

Coronary rotational ablation for calcific coronary artery stenosis in a young child.

Coronary aneurysm formation and subsequent stenosis resulting in ischemic heart disease are the most important complications of Kawasaki disease (KD). Reported is the evolution of severe calcific coronary artery stenosis in an 8-year-old boy managed with percutaneous transluminal coronary rotational ablation (PTCRA) after failed balloon angioplasty. No restenosis occurred 6 months after RA.

Reversal of protein-losing enteropathy with calcium replacement in a patient after Fontan operation.

Protein-losing enteropathy occurs in patients following the modified Fontan procedure. Treatment is still controversial. We describe a boy who developed protein-losing enteropathy 18-months after an extracardiac Fontan procedure.

A rare case of anomalous left circumflex coronary artery from the left pulmonary artery.

The anomalous origin of the coronary artery in children is a rare disease. In particular, an anomalous origin of the left coronary artery from the pulmonary artery is a fatal condition in neonate with myocardial failure. A 46-month-old child with an anomalous origin of the left circumflex artery from the left pulmonary artery was detected due to asymptomatic cardiac murmur and immediately re-implantation of the left circumflex coronary artery was carried out successfully.