An institutional review of sarcomas of the large and small intestine.

Background: This study was done to review the institutional experience with the treatment of sarcoma of the small or large intestine.

Study Design: Thirty-nine patients admitted between the years 1959 and 1987, with a diagnosis of sarcoma of the small or large bowel form the basis of this review.

Results: At referral, 74 percent of the patients presented with peritoneal sarcomatosis.

Thick cutaneous melanoma of the trunk and extremities: an institutional review.

The objective of this study was to review our experience with thick cutaneous melanoma of the trunk and extremities and to identify subgroups of long-term survivors. Ninety-one patients admitted between the years 1977 and 1987, with cutaneous melanoma of the trunk or extremities, Breslow thickness > or = 4.0 mm, or a Clark's level V lesion form the basis of this review.

Metastasectomy in malignant melanoma.

Background: Resection of distant metastases in melanoma is occasionally helpful. The extent of applicability of this treatment, the benefit derived, and the prognostic parameters aiding in the selection of the patients need to be defined further.

Methods: The cases of one hundred fourteen patients with resected distant metastases were reviewed and subjected to multivariate analysis.

Keratosis punctata of the palmar creases. A report on three generations, demonstrating an association with ichthyosis vulgaris and evidence of involvement of the acrosyringium.

Five patients in the same family showed small keratotic plugs of the palmar creases. Transmission in lineage was consistent with an autosomal dominant pattern of inheritance. The syndrome was highly associated with ichthyosis vulgaris in several members of the family.

Electroclinical signs of benign neonatal familial convulsions.

Benign neonatal familial convulsions comprise a distinct epileptic syndrome with an autosomal mode of transmission. The electroclinical signs of seizures in this syndrome are not yet well defined. In 3 children from two families presenting with benign neonatal familial convulsions, 14 seizures were recorded during electroencephalographic (EEG)-video sessions.

Pseudo-Kaposi sarcoma induced by minor trauma in a patient with Klippel-Trenaunay-Weber syndrome.

Arteriovenous malformations (AVM) are vascular anomalies containing a communication between an artery and a vein without an intervening capillary bed. In 1990, Klippel and Trenaunay reported a patient with limb overgrowth, cutaneous angiomata and varicose veins. In 1918, Parkes Weber mentioned the additional feature of AVM terming the condition 'hemangiectatic hypertrophy'.

Agminated blue nevi: case report and review of the literature.

Blue nevi may rarely appear in multiple form and grouped in a circumscribed area, a pattern of arrangement that is more properly designed under the term agminated blue nevi. In this paper a new case with light and ultrastructural studies is described, and the previously reported cases are reviewed. Histologically, there was a characteristic perifollicular arrangement of dermal melanocytes, most of which showed ultrastructurally an extracellular sheath.

Localized familial redundant scalp: atypical cutis verticis gyrata?

Two patients, a mother and son, with a conspicuous redundant unique scalp fold are reported. No underlying disorder was found. Light microscopy was unremarkable.

[Bacillary necrosis in larvae of the bivalve Euvola ziczac (Linnaeus, 1758) caused by a Pseudomonas sp].

The incidence of bacteria as etiological agents of diseases in larvae of bivalve mollusks, is well documented in the literature. In this study, a series of test were performed to identify and estimate pathogenic level of marine bacteria isolated during an epizootic in a larval culture system of the tropical scallop Euvola ziczac. Such bacteria was identified as Pseudomonas sp.

Treatment of unknown primary melanoma.

Sixty-four patients with unknown primary melanoma were identified among 1045 new patients with melanoma (6%) seen during an 11-year period. Their mean age was 44.5 years (median age, 42.

Dandy-Walker malformation: analysis of 38 cases.

Thirty-eight cases of Dandy-Walker malformation (DWM) are presented. A female predominance of 3:1 was found. Thirty-two cases (84%) were diagnosed within the 1st year of life.

Reiter's syndrome and human immunodeficiency virus infection: case report and review of the literature.

The concurrence of Reiter's syndrome and human immunodeficiency virus infection has recently been noted. In this report the evolution of Reiter's syndrome (arthritis, urethritis, and conjunctivitis) in a patient with a history of intravenous drug abuse and positive results of serologic tests for human immunodeficiency virus is described and the literature is reviewed.

Occipital osteodiastasis. A rare complication in cephalic delivery.

A case of occipital bone osteodiastasis in an infant born by cephalic vaginal delivery is presented. Cerebral echography and CT scan did not show posterior fossa haemorrhage. Neurological assessment at three years of age was completely normal.

Prognosis for seizure control in infantile spasms preceded by other seizures.

Thirteen to 43% of patients with infantile spasms (IS) have other types of seizures, which are considered a feature of an unfavourable prognosis and, to some extent, as a contra-indication for steroid treatment. The present series comprised 43 patients treated with steroids, who suffered from other types of seizures prior to IS. The first seizures resulted from 2 different conditions, correlated to a different outcome of epilepsy.

Association between left-handedness and allergy: a reappraisal.

There are conflicting reports in the literature about the possible association between left-handedness and immune disorders, including autoimmune diseases as well as allergies. In this study we compared the distribution of right- and left-handers, assessed with the Edinburgh Handedness Inventory, in a group of patients consulting an allergy clinic and a control population with a similar sex and age distribution. There was no overall association between left-handedness and allergies, although we found a tendency towards left-handedness in patients whose allergic symptoms started before puberty, suggesting that left-handers may have an increased predisposition to allergic disease that manifests itself during early life.

[Ischemic cerebrovascular accidents in childhood].

Authors review 53 children, aged 0 to 14 years, affected with cerebrovascular ischemic strokes. Largest aetiological groups were: a) congenital heart disease, 16 patients; b) arteritis of unknown cause, 11; c) idiopathic arterial occlusion without arteritis images on angiography, 7; d) moyamoya disease, 6; and d) local or systemic infections, 5. The mode of onset was as completed stroke in 72% and stroke in evolution in 24%.